منابع مشابه
Outcome in West syndrome.
OBJECTIVES To assess the seizure and developmental outcome in children with West syndrome with respect to treatment lag. METHODS Twenty-six children satisfying inclusion criteria of West syndrome i.e., infantile spasms, psychomotor retardation and abnormal EEG pattern were prospectively evaluated. Response to treatment was assessed based on seizure control, EEG, developmental assessment and p...
متن کاملWolf–Hirschhorn (4p-) syndrome with West syndrome
Wolf-Hirschhorn syndrome (WHS) is a chromosome disorder (4p-syndrome) which is characterized by craniofacial features and epileptic seizures. Here, we report a case of WHS with West syndrome, in whom the seizures were refractory to several antiepileptic drugs but were responsive to the addition of lamotrigine. The patient had epileptic spasms at age seven months. The interictal electroencephalo...
متن کاملWest Syndrome: Response to Valproate
UNLABELLED Management of West syndrome is unsatisfactory. In our clinic we observed that a significant proportion of patients respond to usual dose of valproate. OBJECTIVE To prospectively assess the efficacy of valproate in controlling infantile spasms in West syndrome. METHODS Consecutive patients presenting with West syndrome to the Pediatric Neurology Clinic or general outpatient depart...
متن کاملBrain connectivity in West syndrome
PURPOSE Hypsarrhythmia, the pathognomonic EEG pattern of West syndrome, is typically characterized by a high amplitude, arrhythmic, and asynchronous pattern. While this severely aberrant pattern would suggest severe abnormalities in connectivity, coherence has not yet been systematically assessed in hypsarrhythmia. METHODS We evaluated the EEGs of 28 infants, 12 with infantile spasms with hyp...
متن کامل[Case of combination of Beckwith-Wiedemann syndrome with West syndrome].
Beckwith-Wiedemann syndrome (BWS) is etiologically connected with genetic/epigenetic growth dysregulation. The supposed localization of this disorder is a short arm of chromosome 11 (11p 15.5). Its prevalence is 1:13 per 700 newborns. West syndrome is an age-dependent epileptic syndrome related to a group of infantile epileptic encephalopathies and characterized by a triad of basic symptoms: se...
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ژورنال
عنوان ژورنال: Journal of Evolution of Medical and Dental Sciences
سال: 2015
ISSN: 2278-4748,2278-4802
DOI: 10.14260/jemds/2015/999